Skip to content

PKU Diet

Make an Appointment

Our team is here to help you make an appointment with the specialists that you need.

PKU Diet

Overview

A low-protein diet is the main treatment for phenylketonuria (PKU). This is because people who have PKU lack an enzyme to properly process the amino acid phenylalanine, a part of protein.

Phenylalanine is present in all protein foods and in some nonprotein foods, such as soda pop and artificial sweeteners. PKU diets typically do not contain high-protein foods such as:

  • Meat, eggs, and fish.
  • Nuts, peas, and beans (and products made from these foods).
  • Milk and cheese.

Read food labels carefully. All foods that contain phenylalanine should have "contains phenylalanine" on the label.

The PKU diet may result in certain nutritional deficiencies that can slow a person's growth. It is important that everyone with PKU sees a specialist for nutritional counseling.

Teach siblings, grandparents, caregivers, teachers, and friends about the dietary restrictions. They need to understand that symptoms of the disease will develop if your child does not follow the diet.

As your child grows, following the diet may become more difficult. Some children may rebel against the diet, especially during the teen years, as they gain more independence and are influenced by peers. Give your child some control by letting your child choose what to eat from a variety of low-phenylalanine foods. Continue to stress the importance of staying with the diet. Explain how straying from the diet can cause both immediate and long-term consequences, such as lower intelligence.

Related Information

Credits

Current as of: September 20, 2023

Author: Healthwise Staff
Clinical Review Board
All Healthwise education is reviewed by a team that includes physicians, nurses, advanced practitioners, registered dieticians, and other healthcare professionals.

This information does not replace the advice of a doctor. Healthwise, Incorporated, disclaims any warranty or liability for your use of this information. Your use of this information means that you agree to the Terms of Use. Learn how we develop our content.